JOURNAL

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About the Authors

Aidana Aubakir – Senior neurologist of the psychoneurological department No. 5 "Balbulak", NJSC "National Center for Children's Rehabilitation", Astana, Kazakhstan, This email address is being protected from spambots. You need JavaScript enabled to view it., ORCID: 0009-0007-9151-8823

Zhadyra Kurmanova – Head of the psychoneurological department No. 4 "Akzhol", NJSC "National Center for Children's Rehabilitation", Astana, Kazakhstan, This email address is being protected from spambots. You need JavaScript enabled to view it., ORCID: 0009-0007-8367-2070

Аbstract

Dyke-Davidoff-Masson syndrome (DDMS) is a rare pathology that refers to atrophy or hypoplasia of one hemisphere of the brain (hemiatrophy), which usually occurs due to a stroke of the developing brain in the fetal or early childhood period. About 10 cases of this syndrome have been described in the world, which classifies it as a rare pathology of the brain. A 7-year-old girl was admitted to our Center for a rehabilitation course under the guise of a diagnosis of "Cerebral palsy", but with symptoms of this rare syndrome, with confirming radiological criteria. We decided to describe this clinical case in detail with an analysis of Dyke-Davidoff-Masson syndrome.

Keywords

Dyke-Davidoff-Masson syndrome, cerebral palsy, hemiatrophy, epilepsy, DDMS syndrome

References

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